Congenital Malformations Registry - 1996 Report
Appendix 4
BPA Codes
Many birth defects registries use a coding system modified from the British Pediatric Association (BPA). This coding system provides more specificity than the ICD-9 system. The Centers for Disease Control and Prevention Metropolitan Atlanta Congenital Defects Program (MACDP) has developed codes that group conditions. The table below shows the MACDP codes and the corresponding BPA and ICD-9 codes. The ICD-9 code may include conditions others than those specified by the BPA code. For example, ICD-9 code 756.7 includes both gastroschisis and omphalocele, but the BPA code allows these conditions to be distinguished.
| MACDP Code | Condition | ICD-9 | BPA 5-Digit Code |
|---|---|---|---|
| CENTRAL NERVOUS SYSTEM | |||
| A01 | Anencephaly | 740.0, 740.1, 740.2 | 740.00, 740.02, 740.03, 740.10, 740.20, 740.21, 740.29 |
| A02 | Spina Bifida with Hydrocephaly | 741.0 | 741.00, 741.01, 741.02, 741.03, 741.04, 741.05, 741.06, 741.07, 741.08, 741.09 |
| A03 | Spina Bifida without Hydrocephaly | 741.9 | 741.90, 741.91, 741.92, 741.93, 741.94, 741.98, 741.99, 742.00, 742.08, 742.09 |
| A13 | Encephalocele | 742.0 | 742.00, 742.08, 742.09 |
| A15 | Hydrocephaly | 742.3 | 742.30, 742.31, 742.38, 742.39 |
| A16 | Microcephalus | 742.1 | 742.10 |
| EYE / EAR | |||
| B01 | Anophthalmia, Microphthalmia | 743.0, 743.1 | 743.00, 743.10 |
| B03 | Glaucoma | 743.2 | 743.20, 743.21, 743.22 |
| B04 | Cataract | 743.32 | |
| B54 | Ear anomaly with hearing loss | 744.0 | 744.00, 744.01, 744.02, 744.03, 744.09, 744.21 |
| CARDIAC | |||
| D01 | Truncus arteriosus | 745.0 | 745.00, 745.01 |
| D02 | Transposition of great vessels | 745.1 | 745.10, 745.11, 745.12, 745.18, 745.19 |
| D03 | Tetralogy of Fallot | 745.2 | 745.20, 745.21, 746.84 |
| D04 | Single ventricle | 745.3 | 745.30 |
| D05 | VSD | 745.4 | 745.40, 745.41, 745.48, 745.49 |
| D52 | Hypoplastic left heart | 746.7 | 746.70 |
| D53 | Total anomalous pulmonary venous return | 747.41 | 747.42 |
| RESPIRATORY | |||
| E01 | Choanal atresia | 748.0 | 748.00 |
| E06 | Agenesis of lung | 748.5 | 748.50, 748.51 |
| CLEFTS | |||
| F01 | Cleft palate | 749.0 | 749.00, 749.01, 749.02, 749.03, 749.04, 749.05, 749.06, 749.07, 749.09 |
| F02 | Cleft lip with or without cleft palate | 749.0, 749.2, 750.5 | 749.10, 749.11, 749.12, 749.19, 749.20, 749.21, 749.22, 749.29, 749.51 |
| GASTRO-INTESTINAL | |||
| F14 | Stenosis or atresia of duodenum | 751.1 | 751.10 |
| F15 | Other stenosis or atresia of small intestine | 751.1 | 751.11, 751.12, 751.19 |
| F16 | Stenosis or atresia of rectum or anus | 751.2 | 751.21, 751.22, 751.23, 751.24 |
| F17 | Hirschsprung's Disease | 751.3 | 751.30, 751.31, 751.32, 751.33 |
| F18 | Malrotation of intestine | 751.4 | 751.40, 751.41, 751.42, 751.49 |
| F21 | Biliary atresia | 751.61 | 751.65 |
| GENITO-URINARY | |||
| H01 | Renal agenesis | 753.0 | 753.00, 753.01 |
| H06 | Obstruction of kidney or ureter | 753.3 | 753.20, 753.21, 753.22, 753.29, 753.40, 753.42 |
| H09 | Bladder or urethra obstruction | 753.6 | 753.60, 753.61, 753.62, 753.63 |
| MUSCULOSKELETAL | |||
| J02 | Curvature of spine (scoliosis or lordosis) | 754.2 | 754.20, 754.21, 754.22 |
| J03 | Dislocation of hip | 754.3 | 754.30 |
| J11 | Arthrogryposis multiplex congenita | 754.89 | 755.80 |
| K01 | Reduction deformity - upper limb | 755.2 | 755.20, 755.21, 755.22, 755.23, 755.24, 755.25, 755.26, 755.27, 755.28, 755.29 |
| K02 | Reduction deformity - lower limb | 755.30, 755.31, 755.32, 755.33, 755.34, 755.35, 755.36, 755.37, 755.38, 755.39 | |
| K05 | Amniotic bands | 658.8 | 658.80 |
| N01 | Diaphragmatic hernia | 756.6 | 756.61 |
| N02 | Omphalocele | 756.7 | 756.70 |
| N04 | Gastroschisis | 756.7 | 756.71 |
| SYNDROMES | |||
| R01 | Down Syndrome | 758.0 | 758.00, 758.01, 758.02, 758.03, 758.04, 758.09 |
| R02 | Patau Syndrome (Trisomy 13) | 758.1 | 758.10, 758.11, 758.12, 758.13, 758.19 |
| R03 | Edwards Syndrome (Trisomy 18) | 758.2 | 758.20, 758.21, 758.23, 758.29 |
| S02 | Fetal Alcohol Syndrome | 760.71 | 760.71 |
| W03 | Conjoined twins | 759.4 | 759.40, 759.41, 759.42, 759.43, 759.44, 759.48, 759.49 |